ʻO ka Bark sarcoma (Ewing's sarcoma) he'ōpū kino ia e ulu ana i ka iwi iwi iwi. Hiki ke waihoʻia i loko o nā iwi o kaʻeke, akāʻo kaʻoi pinepineʻana o kēia maʻi e pili ana i nā iwi lōʻihi, a me nā kāinalua kūlana kiʻekiʻe e ulu pinepine i nā iwi vertebrae, nā iwi a me nā iwi pelvic. Hoʻopili nā iwi o Sarcoma a i ka umauma, i ka moe, i ka'ōpū, aiʻole ka maʻi kanemena.
ʻO nā kumu a me nā hōʻailona o ka sarcoma o nā iwi
ʻO nā kumu no ka uluʻana i ka sarcoma o nā iwi,ʻaʻole i aʻo ponoʻia. ʻO nā mea e kū nei i ka nānāʻana i kēiaʻano o nā maʻi koko e like me:
- nā exostoses cartilaginous;
- nā wāwae;
- ka hoʻohaweweʻana i kaʻili
- ʻO ka maʻi o Paget;
- nāʻano maʻi āpau'ē aʻe.
I ke kumu mua o ka uluʻana o kēia maʻi,ʻaʻohe hōʻailona. Ma hope o ka hoʻomakaʻana o ka ulu e hoʻonui i ka nui, hōʻikeʻia nā hōʻailona o ka sarcoma o ka iwi:
- nāwaliwali o ka iwi;
- ka palena o ka mobility i ka hui, e pili ana i ka'ōpū;
- eha nui loa i ka pō;
- wela.
ʻO ke kiʻi pale iʻikeʻia e ka hyperemiaʻili o kaʻili. Inā he sarcoma male ka mea maʻi, aia kekahi mau hōʻailona o kahi maʻi, e like me keʻano o keʻano o nāʻano pelvic a me keʻano o ka maʻi.
Māmā o ka sarcoma iwi
ʻO ke alakaʻi nui no kaʻikeʻana i ka sarcoma osteogenic o ka wahine, ka humeral a me nā iwi'ē aʻe he aʻo x-ray. Ua hoʻokumuʻia ka hopena hope loa e pili ana i nā hualoaʻa o kahi noiʻi maʻamau o kahi'āpana'ōpiʻi liʻiliʻi, i loaʻa i ka biopsy.
Ma hope o ka weheʻana i ka maʻi, e hoʻomaka koke i ka lāʻau lapaʻau. Hiki ke hāʻawi i ka hōʻailona kūpono no ka sarcoma o ka iwi ma hope o ka hoʻonāʻana a me kekahi mau papa o ka chemotherapy. ʻO ke kumu o kēia maʻi he kiʻekiʻe kiʻekiʻe loa no ka metastasis hematogenous wikiwiki.
ʻO ka'ōpena - ka mālamaʻana i nāʻoihanaʻoihana ke kumu nui o ka hoʻomaluʻana i ka sarcoma iwi o ka lima, ka wāwae, ka pūwae. ʻO nā kuʻikahi no kēlā mau hana he:
- ka pōʻino nui i nāʻiʻo o kaʻiʻo;
- ka komoʻana i ke kaʻina hana kanesa o ka pūʻulu neurovascular;
- ka hōʻoki paʻakikī me ka maʻi kīnā a iʻole kaʻeha o nā kino.
Inā uaʻikeʻia ka nui o ka'ōpona i ka nui o ka nui a iʻole ia mālamaʻia ka hopena me ka hoʻopukaʻiaʻana i ka waihohe a me ka kaheʻana o ka wai, hoʻohanaʻia nā hana hela: amputation and exarticulations.
Hoʻohanaʻia ka hōʻailona no ka sarcoma o ka humeral, hoʻohanaʻia nā femoral a me nā iwi'ē aʻe ke hikiʻole ke hoʻokuʻu i ka'ōpū a me nā kinaseʻa. Pono pono ke hoʻohanaʻia o ka chemotherapy ma mua o ke kahakaha. Hiki iāʻoe ke hoʻoemi i ka nui o ka hana tumo a wehe i ka micrometastases. Eia hou, ua kōkua nā kaʻina hana i ka hoʻoholoʻana inā paʻakikī ka'ōpona i nā lāʻau lapaʻau a koho i ka mālama kūpono ma hope o ka pauʻana o ka hana.
Hoʻoponoponoʻia ka chemotherapy ma muli o ka hoʻopiʻiʻana i ka uluʻana a me ka hoʻopauʻana i nā kineticast microscopic. Hoʻohanaʻia nō hoʻi e mālama i nā metastases lōʻihi i hala mua. Ponoʻia ka hoʻohanaʻana i nā papa he 4-10 me ka hui pūʻia o nā lāʻau lapaʻau e like me:
- Kauhana;
- Inā Ifosfamide;
- ʻO Vincristine;
- 'Ākalapili;
- ʻO Etoposide;
- Cyclophosphamide.
Ka nānāʻana ma hope o ka lawelaweʻana i ka sarcoma iwi
I ka pauʻana o ka mālamaʻana i ke kiʻekiʻe
- Radiography a iʻole CT o nāʻano a pau o ke kāʻei;
- MRI / CT o ka iwi, i hoʻopiliʻia e ka'ōpū;
- Ke kuhi o ka'ōpū .