ʻO nāʻano maʻi maʻi āpau (hemorrhagic) he mea maʻamau i nā lāʻau lapaʻau hou. Ma kahi o 50% o nā hihia heʻano purpura thrombocytopenic, a he nui ka hopena o kēia mauʻano aʻaʻole like i kekahi i kekahi. ʻO kēia maʻi e pili ana i ke kino i nā makahiki.
ʻO ke kino o ka Thrombocytopenic - kumu
ʻO ka Verlhof maʻi a iʻole ka thrombocytopenic purpura,ʻaʻole iʻike nuiʻia nā kumu o kēia wā a hiki i kēia manawa - he mea iʻikeʻia e kahi mea'ikekema German i ka makahiki 1735. I loko o ka poʻe, ua kapaʻiaʻo ia he "maʻi kūmā" no ka mea i loko o kēlā mau maʻi i ka mahele o ke kino maʻaneʻi a ma laila eʻikeʻia nāʻano o nāʻano he nui.
ʻO ka maʻi, i ka hapanui o nā hihia, ke hanaʻia ma nā keiki mai ka hānauʻana a hiki i ke'ōpiopio, a laila hiki ke hemo wale keʻole ma waho o nā hana hoʻopiʻi. Ma nā keiki i lalo o kaʻelua o nā makahiki, ua kākau pinepineʻia nāʻano o ka'ōpala ma nā keikikāne. I ke kanaka makua, ua hanaʻia kēiaʻikepili i 1-13 mau maʻi o ka 100,000 mau kānaka, aʻo ka hapanui o nā hihia he wāhine.
Nāʻano o ka purpura thrombocytopenic
ʻO kahi maʻi koko e like me ka purpura thrombocytopenic (ke maʻi o Verlhof) ke pukaʻia nā wā o ke koko - nā platelet, e ko lākou kino pono'ī a make mua. ʻO ka manawa o ko lākou ola ma kahi o 7-10 lā, he mau hola. No ka hanaʻana i nā mea hakakā autoimmune, he kuleana ke koʻikoʻi. ʻO ka maʻi he mauʻano likeʻole e hilinaʻiʻia ma ke kumu o ka maʻi, akā heʻano liʻiliʻiʻole ma nā maʻiʻai:
- autoimmune aiʻole idiopathic;
- heteroimmune;
- ka transimmune.
Ke māheleʻia nāʻano o ka purīpīpīsciopic idiopathic, me ka nānāʻole i nā kumu, i loko o:
- kaʻoi;
- Hōʻalo (me ka pinepine, ka hopena a iʻole ka hoʻomau pinepine).
Hoʻomaʻemaʻe kūponoʻo thrombocytopenic
I kekahi mau kumu, hoʻomaka ke kino e hana iā ia iho. Heʻano likeʻole kēia o ka maʻi. Hoʻopauʻia nā plaletlets e ka'ōnaehana kamepiula, aʻikeʻia iā lākou he mau pūnaewele'ē aʻe. ʻO kēiaʻano maʻi i kekahi manawa ke kū'ē i ke kūlana o kekahi kaʻina hana autoimmune ma ke kino. ʻO keʻano o ka hoʻomaʻemaʻe kūlohelohe o ka thrombocytopenic i ka lukuʻiaʻana o kona mau peleti pono'ī ma lalo o ka mana o nā kumu. I kekahi manawa heʻano maʻi pilikino kēia, akā ma ka hapanui o nā kumu, nā kumu o kēia maʻi:
- lupus erythematosus pūnaewele ;
- anemia hemolyune autoimmune;
- nā vasculitis maʻi ;
- ka maʻi leukemia līpī;
- ia hepatitis;
- keʻano o glomerulonephritis .
ʻO ka Heteroimmuneʻo ka pulpura thrombocytopenic
Ma ka wā kamaliʻi,ʻo ka heteroimmune (non-immune) o ka maʻi, heʻano pulupolic thrombocytopenic ka hopena,ʻoi aku ka nui o nā manawa ma mua o nā mākua. ʻO ka'euakai maikaʻi, he maikaʻi ka hoʻomaʻamaʻaʻana o nā keiki. ʻO nā kumu o kēia maʻi:
- lawe i kekahi lāʻau lapaʻau (paracetamol, furosemide, quinine, ampicillin, cephalosporins, betta-blockers, a pēlā aku);
- immunization (vaccination with BCG, cough, cough, poliomyelitis);
- maʻi.
ʻO ke kino o ka Thrombocytopenic - hōʻailona
ʻO ka maʻi o Verlhof,ʻo kona mau hōʻailonaʻano maʻalahi loa, e like me ka manawa o keʻano o ka hemorrhages. ʻO keʻano, i ka hoʻomakaʻana, nāʻeha a, paha i kapaʻia e nā kauka - petechiae, i kaʻoluʻolu loa, ho'ēmi haʻahaʻa i ka lahilahi o ka laulā a lilo i loko o ka cyanotic,'ōmaʻomaʻo, a me keʻano melemele. I kekahi manawa i ka manawa, hiki i nā kino a pau ke kū i ke kino,ʻo ia ke kiʻi weliweli, akāʻaʻole lākou iʻeha, kahiʻole heʻeha o ka hopena o kahi kanaka ola.
ʻO ka'ālīpiʻi aia ma nā lālā, ma ka liʻiliʻi ma ke kino, a heʻano paʻakikī, akāʻo ka mucous wale nō. Heʻano likeʻole nāʻano o keʻano o ka pulpura o Thrombocytopenic ma nā poʻe'ē aʻe. Hiki iā lākou ke ala aʻe ma muli o ka microtrauma, a me ke kumuʻole. ʻO ke kumu,ʻo ka hanuʻana i ka pō. I kēia hihia,ʻaʻole ka mea maʻi i loaʻa i kaʻeha, koe wale no ka hemorrhage āpau, i ka manawa e makemake nui ai ka mea maʻi i ka hoʻomaha. Hoʻokaʻawale:
- kahe mucous kahe (mai ka ihu,'ākau, kōpū);
- ke kahe i loko (ka'anakalino, ka nui, ka ophthalmic, cerebral).
Ka hōʻoiaʻana o keʻano o ka pulpura thrombocytopenic
ʻO ka maʻi Verlhof, ka mea iʻikeʻoleʻia me kaʻike o nā hōʻailona, ma muli o nā hopena o nā hoʻokolohua hoʻokolohua e pili ana i nā maʻi a me ka hoʻokolokoloʻana. Hoʻomaʻamaʻa nā kauka i ka hana me keʻano o ke kino o ka'ōhuma thrombocytopenic no ka manawa mua. Ma hope o kaʻikeʻana o nā maʻi kūlike aʻikeʻia nāʻano likeʻole mai ka laweʻana i ke koko no ka hoʻowākino, ma mua o ka hoʻokōʻana i nā hoʻouluʻana o ka maʻi. Eia kēia mau mea:
- ʻO ka ho'āʻoʻana i ke kuʻiʻana, i ka manawa e hoʻokomoʻia ai ke kīpili no ke ana i ke kaumaha no 10 mau minuke. Inā ma ka hopena o kēia manawa he mau koko koko i hanaʻia ma lalo o ke kīpili, pono ka pahuhopu. Hanaʻia ia i loko o nā keiki mai ka makahikiʻekolu.
- Hoʻopiliʻia ka ho'āʻoʻana i ka hoʻohanaʻana o kahi kauka lāʻau i ka lima, a ma hope iho o ka manawa e hoʻopiʻiʻia ai kahi paopao - ua kūpono kēia ala no nā mea maʻi.
ʻO ke kino o ka Thrombocytopenic, hoʻopukaʻia kekahi mau ho'āʻo e hōʻike i kahi hilinaʻi kūpono o ke koko o ka mea maʻi. Loaʻa kēia mau ho'āʻo koko no:
- hemoglobin;
- ke kahe o ke koko;
- ke kiʻekiʻe o nā platelets;
- ka heleʻana a iʻole ka puka hou o kaʻeha koko;
- ka mua o nā antiplatelets i loko o ke koko.
Eia kekahi, i nā hihia koʻikoʻi a iʻole ka hilinaʻiʻole i nāʻano likeʻole o ka hōʻoia o ka pulpura thrombocytopenic, hoʻokōʻia ka biopsy o ka iwi - trepanabiopsy. Me ke kōkuaʻana o kahi mea hana hoʻolālā kūikawā, ua hanaʻia kekahi punana liʻiliʻi o ka'ōiwi ma ka'āina lumbar e lawe ai i kahi liʻiliʻi o nā iwi āpau, ka periosteum a me ka wai o ka'ōpala no ka hōʻailona.
ʻO ke kino o ka Thrombocytopenic - ka mālama
ʻO nā maʻi koko ke koi aku i keʻano koʻikoʻi, no ka mea,ʻo ka olakino o ka mea maʻi i kēlā me kēia makahiki e hilinaʻi nui ia ma kēia. Hoʻomaʻaʻia keʻano o ke kino o ka thrombocytopenic ma ka haukapila (i kahi manawa o ka exacerbation) a ma ka home. Pono ia e hoʻolako i ka mea maʻi me ka hoʻomaha nui a me ka moe e hoʻomaha no ka hoʻemiʻana i ka helu o nā manawa traumatic. Ma muli o kēia kūlana, ua hoʻohanaʻia nāʻano hana lāʻau kahiko me ka lāʻau lapaʻau. He mea nui loa ka mālamaʻana i kekahi meaʻai.
Pehea e ola ai ka maʻi o Verlhof?
Ma muli o ka makahiki a me ka manawa hea iʻikeʻia ai ka maʻi Verlhof, e nīnauʻia ana kona kūpaʻa. I ka wā kamaliʻi, he kūpono ke prognostic, keʻikeʻia ka pēpē i ka wā mua a ua mālamaʻia i loko oʻeono mahina. Ma hope o kēia manawa, hiki ke wehewehe i ka hōʻailona, aʻano like me ka thrombocytopenia hemorrha.
Ua pōmaikaʻi nā mākua - hiki ke kū i kēia kūlana me lākou i ko lākou ola a me nā manawa o ke kalaʻia a me ka hōʻalo. I kekahi mau kumu, hiki ke mālama i ka purpura thrombocytopenic maʻamau i ka wā i hoʻoneʻeʻia ai ke kui, akāʻaʻole kēia e hōʻoia 100%. Hoʻopau kēia'ōpū i nā pāʻani pōhaku aʻo ia kaʻenemi o ke kino. Hoʻohanaʻia ke alahana e like me ka hoʻopiʻi hope, i ka wā iʻole ai nāʻano likeʻole. Hoʻohanaʻia ma keʻano heʻano cavitary, a me ke kōkuaʻana o ka laparoscopy.
ʻO ke kino o ka Thrombocytopenic - mau lāʻau lapaʻau
ʻO ka pahuhopu o keʻano o ka mālamaʻana i ka maʻi Verlhofʻo ka mālamaʻana i ke kiʻekiʻe o nā platelets i loko o ke koko ma kahi i makemakeʻia. Hoʻomaopopoʻia ka hoʻomaʻemaʻe kumupiʻi thrombocytopenic kūlohelohe, ma ka hapanui o nā kūlana i kūpono, a hiki i ka loaʻaʻana o kahi kalahala pale no nā makahiki he nui. Ināʻaʻohe kōkua a me ka lawelaweʻana, ua hoʻololiʻia ke kumukūʻai no ka lāʻau lapaʻau i mea hou. No ka hanaʻana i kēia, hoʻohana:
- ʻO Prednisolone (Methylprednisolone) he lāʻau hoʻohāmoku steroid-i loko o ka lāʻau, e ho'ēmi i ka hana o ka pāʻani. Hoʻohanaʻia ia i nā papa mua o ka lāʻau lapaʻau, ma mua o ka weheʻiaʻana o ke kau.
- Hoʻohanaʻia Interferon a2 e kāohi i kona mau pono'ī palepili, i ka wā e hikiʻole ai i nā lāʻauʻaeʻa steroid ke mana.
- Hanaʻia ka Immunoglobulin G ma mua o ke kahakahaʻana e hoʻonui i ke kiʻekiʻe o nā platelets.
- Ke hoʻohanaʻia nā Immunosuppressants (Cyclophosphamide, Vincristine a me Azathioprine) i ka manawa eʻikeʻole ai ka mea maʻi i kekahi hana'ē aʻe. Aia i kahi hoʻomalu o nā pūʻali i loko o ke koko, e hoʻonui ana i ka nui o nā platelets.
- ʻO ke kau lāʻau Danazol, e hoʻonāukiuki i ka'ōpū pituitary me kahi lōʻihi lōʻihi e pili ana i ke kiʻi o ke koko.
ʻO ke kino o ka Thrombocytopenic - mālamaʻia me nā lāʻau lapaʻau
ʻO keʻano o ke kino o ka thrombocytopenic ka maʻi koko, a no laila, ua hoʻohana maikaʻiʻia nā papa lāʻau lāʻau me nā mea hemostatic no kona mālamaʻana:
- nettle nettle;
- he koko-'ā'ī;
- ke kolaʻeleʻele;
- kāhili;
- he kiake hipa;
- chamomile;
- kalola.
ʻO kaʻai me ka purpura thrombocytopenic
ʻAʻoheʻai maʻamau no ka maʻi o Verlhof. He mea nui e hoʻohanaʻia nā pā i kahiʻano mahana a maikaʻi. ʻO nā hua kanu laulā me ka purpura thrombocytopenic, e like me nā hua he mea maikaʻi loa akāʻaʻole pono lākou e hana i nā meaʻaeʻa. ʻO ka papa inoa o nā huahana i'ōleloʻia:
- porridge - buckwheat, kānana, oatmeal;
- nā huaʻona a me nā mea kanu i keʻano o nā wai - kāloti,'ōlaʻi, pīpī, pomegerane,'ōmato;
- nā hua - nā currants, nā lāʻau'ulina, nā huapona;
- ka iʻa;
- kaʻiʻo - pipi.
Pono pono e hoʻokaʻawale i kaʻai:
- nā huahana paʻakai;
- nā mea i puhiʻia;
- nā mea kanu a me nā meaʻala;
- nā'ō lauʻona;
- nā huahana wikiwiki;
- nā mea inuʻona;
- kapala;
- ka waiʻona.
ʻO ke kino o ka Thrombocytopenic - pilikia
ʻO ka maʻi o Verlhof, ka meaʻoi loa o ka pilikia, pono ke koiʻana i ke olakino. Loaʻa nā hōʻailona:
- ka hōʻaha kalapila;
- ka lāʻauʻokoʻa a me ke koko;
- ka nui o ka hanu menstrual i ka wā'ōpiopio.
ʻO ke kino o ka Thrombocytopenic - ka pale
Keʻikeʻia ka mea maʻi i ka "purpura thrombocytopenic,"ʻo ia hoʻi, no ka pono o kona olakino pono'ī e hāʻawi i nā hana he nui, nā meaʻino a me nā mea maʻamau, keʻano o ka nohona ola. Hoʻolālāʻia nā hana hoʻolālā e mālama i ke kiʻekiʻe o nā platelets a me ka hemoglobin no kaʻaiʻana, a me ka hoʻoneʻeʻiaʻana o nāʻano koʻikoʻi:
- ʻauʻau;
- 'ōlohelohe;
- ka meaʻai maʻamau no ka pohō kaumaha;
- nā pilikia.