ʻO ka maʻi o Werlhof -ʻo ka pulpura thrombocytopenic - kahi maʻi i hōʻikeʻia i keʻano o nā maʻi hemorrhagic e pili ana i ke kumu o ka hoʻonuiʻiaʻana o nā platelets. Hoʻopiliʻia ka microthrombi i nā kukui o nā liʻiliʻi liʻiliʻi. Eia kekahi, he hoʻoheheʻeʻia nā pūpū koko a me ka emiʻana o ka helu o nā platelets.
Nā kumu o ka maʻi o Werlhof
I kēia manawa,ʻaʻole iʻikeʻia nā kumu kūpono o ka purpura thrombocytopenic. Hoʻoholo i nāʻano kula kiʻekiʻe a me ke kula kiʻekiʻe o ka maʻi o Verlhof. ʻO nāʻano papa mua he laikini ma keʻano a iʻole ka hōʻailona ma muli o ka maʻi maʻi. ʻO nā pukaʻelua he mau hōʻailona o nā maʻi.
Nā Hōʻaia o ka maʻi o Verlhof
Hoʻomaka ka maʻi i ka maikaʻi, no ka meaʻaʻole kumu kūpono, i kekahi manawa e pili ana i nā maʻi o ka'ōpū a me ka ARI. I ka mea hoʻomanawanui i ka pae mua, hiki keʻikeʻia nā hōʻailona o kēia mau hiʻohiʻona:
- wela;
- kahe (vomiting lua);
- nā maʻiʻeha;
- ka nawaliwali nui, ka luhi;
- i kaʻeha ma ka umauma a me ka'ōpū.
ʻO ka hōʻailona nui he hōʻino a me nā hemorrhages subcutaneous, e wehewehe ana i ka inoaʻelua o ka maʻi - thrombocytopenic purpura.
Ma hope o ka manawa pōkole, hōʻike ka maʻi hemorrhagic iā ia iho ma keʻano o:
- ka'ōpū, ka maʻi koko, a me nā wāhine pūpū;
- nā huehe kaheʻana , nā pēpi mucous;
- ka hemorrhages ma ka liʻiliʻi o ka maka;
- hemoptysis.
Hōʻike pūʻia nā hōʻike hemorrhagic e nā maʻi neurological, e like me:
- hoʻomaha;
- hiamoe;
- ka wehewehe i ka manawa a me ka manawa;
- ua emi iho kaʻike;
- ʻO ka paralysis pākahi.
I nā hihia koʻikoʻi, hiki iā ia ke hoʻomohala i kahi coma.
He nui nā hemorrhages ma lalo o kaʻili a noho i kahi ākea nui. Ma muli o ke kaupiliʻana, heʻalohi kaʻeleʻele mai kaʻulaʻula-keʻokeʻo i ka melemele (e like me kaʻehaʻeha).
ʻO ka hōʻailona o ka maʻi a Verlhof e hoʻomaka me ka hōʻailona a me ka hana hana a ka mea maʻi. Aia nā maʻi hōʻailona i nā ho'āʻo o kēia mau mea:
- Ke ho'āʻo nui o ke koko ('OAK). Hoʻoholoʻia ka maʻi ma o ka hoʻohaʻahaʻaʻana i ka kiʻekiʻe o erythrocytes a me hemoglobin, e ho'ēmi ana i ka helu o nā platelets a me kaʻikeʻana i nā'elepelu antiplatelet.
- Ka hoʻopaʻi pale - e lawe i ka iwi o ka iwi no ka ninaninauʻana ma o ka hopena sternum. Ma ka hoʻonaʻauaoʻana i keʻano o ka mīkini, hiki ke piʻi i ka helu o megakaryocytes, he wahi liʻiliʻi o nā platelets, akāʻaʻole he mau hoʻololi'ē aʻe i loko o ka iwi o ka iwi, no ka mea, heʻano kūpono o ka hoʻokumuʻana i ka tumo.
- ʻO Trepanobiopsy - he haʻawina o ka iwi iwi a me ka iwi (mai ke pelvic region), i laweʻia me ke kōkuaʻana o kahi lāʻau lapaʻau o ke kao. Me ka maʻi o Verlhof,ʻo ka lakene o ka momona o ka iwi momona a hematopoietic e like me ka mea maʻamau.
Hanaʻia o ka maʻi o Verlhof
Hoʻopili nā mea lapaʻau e pili ana i keʻano o ia maʻi. Hoʻomaʻiʻia nā hōʻailona e kekahi o kēia mauʻano:
- ʻO ka hoʻohanaʻana i nā corticosteroids no ka hopena o ka hopuʻana i ka maʻi hemorrhagic a me ka hoʻonuiʻana i ke kiʻekiʻe o nā platelets i loko o ke koko. Hoʻonohonohoʻiaʻo Prednisalon i kahi likelika he 1 mg no 1 kg o ka maʻi paʻi i kēlā lā i kēia lā. I ka hihia o ka maʻi, e hoʻonuiʻia ka uku.
- Ināʻaʻole i hoʻokōʻia ka mana pono, pono ka mea maʻi e hoʻokuʻu i ka'ōpū . Wahi a nāʻike helu lāʻau, i ka 80% o nā maʻi ma hope o ka lawelaweʻana i ka hananaʻana o ka hananaʻana.
- I nā mea koʻikoʻi, ma hope o ka splenectomy spineen, kahe e kahe, a hoʻomauʻia ka maʻi, ua kauʻia nā immunosuppressants (Azathioprine, Vincristine) a me glucocosteroids.
No ka weheʻana i nā hōʻailona o waho o ka maʻi hemorrhagic, hoʻohanaʻia nā mea hoʻohana haemostatic:
- Adroxon;
- ʻAi;
- ʻO ka'ōpū Hemostatic;
- nā hua'ōnerogene.