ʻO ka maʻi Hirschsprung he aganglion o ka pūpū nui. ʻO ka mea maʻiʻole he mau pūnana nerve i loko o ka plexus submucous o Meissner a me ka plexus muscle o Auerbach. Ma muli o ka nele o kekahi mau hihia ma ka wahi i hoʻopiliʻia a hoʻolōʻihi lōʻihi i ka waihona i loko o nāʻoihana'ē aʻe, aia i ka lōʻihi a me ka hoʻonuiʻana o ke kui.
Nā hōʻailona o ka maʻi o Hirschsprung
ʻO nā hōʻailona mua loa o ka maʻi o Hirschsprung, he lapalapa o ka maʻi, constipation a me ka piʻiʻana o ka'ōpū o ka'ōpū. Inā 'aʻole e nīnau ka mea maʻi i ke kauka, hiki mai nā hōʻailona o ke kau. Eia kēia mau mea:
- anemia ;
- hypotrophy;
- nā pōhaku momona.
I kekahi mau kumu, loaʻa nā maʻi i kaʻeha i loko o ka'ōpū, hiki i ka ikaika ke hoʻonui i ka lōʻihi o ka lōʻihi.
Nā kūlana o ka maʻi Hirschsprung
Ke ulu nei ka maʻi o Hirschsprung i nā hanana. ʻO ka māhele mua loa o ka maʻi i ukuʻia:ʻo ka mea maʻi ka constipation, akā no ka manawa lōʻihi, hiki i nāʻenemi hoʻomaʻemaʻe ke maʻalahi ke hōʻoki.
Ma hope o kēia, hiki i kahi hanana hoʻokūkū, i ka manawa e kaumaha ai ka maʻi o ka mea maʻi a me kaʻenemi. I kēia manawa i ka uluʻana o ka maʻi o Hirschsprung i ka poʻe mākua, paʻakikī ke kaumaha o ke kino, hopohopo lākou i ka kaumaha ma ka'ōpū a me keʻano o ka hanu. I kekahi mau kumu, uaʻikeʻia ka maʻi anemia maʻamau a me nā maʻi kūmole.
ʻO ka wā aʻe o ka maʻi i hoʻokaʻawaleʻia. ʻAʻole kōkua nā maʻi i nāʻenemi hoʻomaʻemaʻe a me nā laxatives. Ke kaumaha neiʻo ia i loko o ka'ōpū lalo, a ua hoʻomaka koke ka hanuʻana i ka'ōpū.
ʻO ka hōʻoiaʻana o ka maʻi o Hirschsprung
Inā loaʻa ka manaʻo kānalua o ka maʻi o Hirschsprung, e hana muaʻia ka hoʻokolokolo maʻamau. Ma mua o ke ahulau, loaʻa kahi ampoule liʻiliʻi o ka'umekau i ka mea maʻi. Hoʻonuiʻia ka leo o ka sphincter. I kēia hihia, pono e hanaʻia kekahi leka uila o nā mea a pau o ka lua o ka'ōpū. Me ka maʻi o Hirschsprung, ua hoʻonuiʻia a me ka hoʻopihaʻia nā puka o ka pā, kahi manawa eʻike ai i nā wai.
Pono nō ka mea hoʻomamāwanui e hoʻokomo i kahi hōʻailona sigmoidoscopy, pilikino, colonoscopy a me nā diagnostics histochemical.
Hanaʻia o ka maʻi o Hirschsprung
ʻO ke ala wale nō e hana ai i ka maʻi o Hirschsprung. ʻO nā kumu nui o ka hana:
- ka hoʻolimalimaʻana o nāʻoihana i hoʻonuiʻia;
- ka hoʻoneʻeneʻeʻana o ka'āpana o nā aganglionic;
- ka mālamaʻana i ka māhele o ka pūpū nui e hana.
No nā kamaliʻi, ua hoʻokumuʻiaʻo Swanson, ko Duhamel, a me Soave e hana i nā hana ho'ōla. ʻO nā mākua i kā lākou hana ma keʻano maʻamau, ua hōʻokiʻia ma muli o nā hiʻohiʻona anatomical a me ka sclerosis paʻakikī ma nā maʻi muscular a i lalo o nā'ōpū. Ma ka pinepine, me ka maʻi o Hirschsprung, ua hoʻololiʻia ka hana a Duhamel, kahi i hoʻoneʻeʻia ai ka'āpana o nā mea āpau me ka hanaʻana i kahi pou pokole o ka pāʻani. I ka hapanui o nā hihia, hiki ke pale i kaʻino o ka sphincter o ka anus a hana i ka anastomosis colorectal.
Ma mua o ka hanaʻana, pono ka mea maʻi
ʻO ka hōʻailona holomua no ka maʻi o Hirschsprung ma hope o ke kāpiliʻana. Akā, i kekahi mau mea, hiki ke koiʻia ke kuhi hou. ʻO ka wā mau loa keʻano o ka hanaʻana o ka hanaʻana i ke kūkulu houʻiaʻana o ka anastomosis a ke mālamaʻia nei ma o ka peritoneal a iʻole ka perineal.