ʻO kahi'ōpiko paʻakiki i loaʻa ma kahi o nā āpau a me nāʻanoʻano'ē aʻe paha o ka pūʻali pūpū i kapaʻia he pheochromocytoma -ʻo nā hōʻailona o kēia maʻi e hōʻike ana i ka hana hoʻonanea o ka neoplasm. Aia i loko o nā pūnaewele o kaʻiʻo chromaffin a me ka waiwai o ka lolo. ʻO nā maʻiʻeha o kēiaʻano he lapuwale, ma 10% wale nō o nā hihia.
Pheochromocytoma - kumu
ʻAʻoleʻikeʻia ke kumu e ulu ai kēia maʻi. Aia kekahi mau manaʻo e hōʻikeʻia ka neoplasm ma muli o ka hoʻololiʻana o ka hoʻohui.
ʻO ka hapanui o ka maʻi e pili ana i nā poʻe ma ke kinoʻana, mai 25 a 50 mau makahiki, he nui nā wāhine. ʻO ka haʻahaʻa, ulu nui ka'ōpū i loko o nā keiki, a ma ka hapanui o nā manawa, aia i loko o nā keikikāne.
Ke hui pinepineʻia ka pheochromocytoma me kekahiʻano o ke kanesa (thyroid, hanu, mucous membranes), akā,ʻaʻole kūpono nā kinakoki.
Nā hōʻailona o ka pheochromocytoma
Hoʻokumu ponoʻia ka'ōpipōpona ma kahi o ka piko, no ka mea,ʻo ke koko o ka'ōpū o ke adrenal ka mea e loaʻa ai iʻeluaʻano o nā hormones: adrenaline a me norepinephrine. I nā kumu'ē aʻe, hiki i nā norepinephrine wale nō. A laila, eʻike nuiʻia ka hopena o ka pheochromocytoma me kona wahi kūpono.
Eia kekahi, heʻokoʻa keʻano o nā hōʻailona no nāʻano iʻikeʻia o ka maʻi, i hoʻolālāʻia e like me keʻano o ka maʻi:
- paroxysmal;
- pinepine;
- i huiʻia.
Paroxysmal pheochromocytoma - hōʻailona:
- ʻo ke kumukūmālua o Carney (hoʻopau o ka naʻau, hoʻonui i ka wela, ka maʻiʻeha);
- piʻi nui a me ka hikiwawe i nā kīʻaha ke koko i 300 mm Hg. Nā'Ōlelo. aʻoi aku;
- pallor;
- heʻano makaʻuʻole o ka makaʻu;
- nā mea nui;
- ka eha ma ka'ōpū a ma hope o ka sternum;
- pōkole o ka hanu;
- nausea;
- polyuria;
- ʻike pōʻino;
- piʻi ka mahana;
- luaʻi.
ʻO keʻano mau o ka'ōpū e hōʻikeʻia ana e ka uluʻana o ka ikaika a me nā hōʻailona e like me keʻano o ka maʻi nui.
ʻO ka neoplasmʻano maʻalahi ke kumu o ka pilikia nui - me ka pheochromocytoma hiki iā ia ke alakaʻi i ka hemorrhage nui i loko o ka peni o ka maka, ka edema pulmonary, aiʻole ka hahau.
Pheochromocytoma -ʻikeʻike
Ua hanaʻia ka weheweheʻana ma hope o ka nui o nā hoʻokolohua leaka uila:
- ke aʻoʻiaʻana o ke koko no ka mālamaʻana i nā catecholamines, ke kūʻana o ka leukocytosis, hoʻonuiʻia ka ESR, hyperglycemia, erythrocytosis, eosopopialia;
- ka wikiwiki no kaʻike o cylindruria, proteinuria, glucosuria, excretion o ka vanillylmandelic acid;
- nā hōʻike hana me ka histamine a me ka hoʻoponopono.
Hiki ke loaʻa hou aku nāʻike hou ma o nā ultrasound of gland , nā palapala i kākauʻia, ka pilikino, ka scintigraph.
Pono e hoʻomaopopoʻia i ka manawa o ka pheochromocytoma e lōʻihi ai ka manawa eʻike ai i ka maʻi i ka manawa a hoʻomaka ke kaohi. No laila,ʻo kēlā me kēia mea e loaʻa ana i ke koko kiʻekiʻe, pono ia e lawelawe i kekahi loiloi lāʻau no ka weheʻana i ke koko i nīnauʻia he kumu no ka hoʻonuiʻia o ke koko.
Pheochromocytoma - nā pilikia a me ka hōʻailona
ʻO ka hapanui o nā hopena hopena maikaʻiʻole ma hope o nā pilikia:
- 'eeʻole i ke kīnā;
- ua pilikia ka hanuʻana o ka lolo;
- 'ōmaha pulmonary ;
- ka naʻau pilikia.
I ka neleʻana o nā lāʻau lapaʻau kūpono, pono nā maʻi, e make.
ʻO ka hoʻoukaʻana a me ka weheʻana o ka pheochromocytoma hiki i ka hoʻokōʻana i kahi hōʻailona kūpono, keʻole ināʻaʻoleʻino ka'ōpū aʻaʻohe he kūpono. E like me ka hōʻikeʻana, hōʻikeʻia nā kuhiʻana i 5-10% wale nō o nā hihia, a ua hoʻoponopono ponoʻia nā koena i ke kōkuaʻana o nā lāʻau.