ʻO ka maʻi, ka mea e hoʻonui i ka paia o ka hema, a ma nā meaʻoi loa o ka ventricle pono o ka puʻuwai, ua kapaʻiaʻo ka cardiomyopathy hypertension (HCMC). I loko o kēia maʻi, hoʻomāhuahua ka nui o nā hihia maʻamau, a no laila keʻeha mau nei ka septum hihia.
Manaʻoʻia he maʻi kēia o nā mea pāʻani - no ka hoʻonuiʻana i ka ikaika e hanaʻia ai ka maʻi koko. Uaʻike mua mākou i kekahi mau hihia i ka wā i make ai nā kānaka pāʻani ma ke kahua pāʻani ma muli o keʻano o ka maʻi cardiomyopathy - ka mea hoʻokani pôpeku Hungarianʻo Miklos Feher a me ka meaʻelimaʻo Jesse Marunde.
I loko o kēia maʻi, he wahi chaotic ka paʻakai i loko o ka myocardium, kahi e pili ana i ka hoʻohuiʻiaʻana o ka hua.
Nāʻano o ka maʻi o ke koko
I kēia lā,ʻikeʻia nā kauka e 3 mauʻano o ke kāpikipipiki o ke koko:
- Palekana Basal - hoʻonui ka hoʻomaha ma mua o ka 30 mm Hg. Nā'Ōlelo.
- Ka lapaʻau o Labile - uaʻikeʻia nā hanu holoʻokoʻa o ka māmāʻokoʻa.
- Hoʻopilikia pa'ū - kahi māmā ma kahi mālie ma lalo o 30 mm Hg. Nā'Ōlelo.
ʻO kaʻaeʻana i ka hyperterpic cardiomyopathy e pili ana i kēia mauʻanoʻekolu o ka maʻi,ʻoiai heʻanoʻoʻoleʻaʻole keʻano o keʻano e hōʻikeʻia ana e ka māmā lahipine ma lalo o 30 mm Hg. Nā'Ōlelo. ma kahi hoʻomaha a hoʻonāukiuki.
Nā hōʻailona o ka hypertrophic cardiomyopathy
Hōʻalowale ka Symptomatic o ka hypertrophic cardiomyopathy - ma kahi o 30% o nā mea maʻi e hanaʻole i nā hoʻopiʻi, i ia manawa e lilo koke ka make i ka hōʻike wale nō o ka maʻi. Ma kahi kūlana kūikawā, he mau'ōpiopio'ōpiopio iʻole e nānā i ka hoʻopiʻi, koe wale no ka hoʻopilikia o ka naʻau.
ʻO kēia maʻi ka mea i kapaʻia e ka maʻi liʻiliʻi liʻiliʻi - ma kēia hihia, kaʻehaʻeha, kaʻuʻuku o ka hanu a me ka uhuki, a me nā hanana angina .
Eia kekahi, me keʻano o ka cardiomyopathy hypertrophy, hiki i nā hōʻike o ka hāʻuleʻole o ka puʻuwai ventricular hema, e hiki ai ke ulu i ka hanu naʻauʻole.
ʻO nā hemahema i ke kani o ka puʻuwai e hiki ai ke hōʻeha . ʻO ka manawa kēia he mau extrasystoles ventricular a me paroxysms o ka tachycardia ventricular.
I nā hihia maʻamau, hiki i nā maʻi ke loaʻa i ka maʻi endocarditis a me ka thromboembolism.
ʻO ka hōʻoiaʻana o ka hypertrophic cardiomyopathy
Ma waho o nāʻano likeʻole o ka cardiomyopathy, uaʻikeʻia kaʻano maʻalahi o ka pepa hypertrophic ma muli o ka hōʻaiaʻana: no ka hōʻoiaʻana o ka hōʻailona,ʻoi aku ka nui o ka myocardial ma mua o ka 1.5 cm a me ka waihoʻana o ka maʻi hemahema (left impairment).
Ke nānāʻia, hiki i ka mea maʻi ke hoʻonui i ka palena o ka naʻau i ka hema, a i ka wā e paʻiʻia, loheʻia ka leo (systolic rhomboid).
Ma waena o nāʻano'ē aʻe o ke aʻoʻana i kēia mauʻano pilikino, penei:
- electrocardiography - me ia eʻike ai lākou i ka hoʻonuiʻana ma ka hema hema;
- ʻO ka'ōlohelohe keʻano nui e kōkua i ka huliʻana o ka hypertrophy;
- Mālama mālama ECG - e hoʻoholo i ka haunaele;
- kiʻi kiʻi kūhoho - hoʻohanaʻia e like me keʻano hoʻomaʻemaʻe;
- ʻo ke diagnostics genetic kekahi o nāʻano nui no ka loiloiʻana i ka maʻi hōʻailona.
ʻO keʻano o keʻano o ka maʻi
ʻO ka hōʻailona a me ka mālamaʻana i ka maʻi diabolic cardiomyopathy e pili pono ana ia e pale ai i ka hopena hopena. Ma hope o ka noʻonoʻoʻana i ka hōʻailona o ka maʻi, inā loaʻa kahi hopena hopena, hanaʻia ka hana maʻalahi. Ināʻaʻohe makehewa make, aʻaʻohe hōʻailona
No ka mālamaʻana, he mea nui ka kaohiʻana i ke kino, a me ka hoʻohanaʻana i nā lāʻau lapaʻau me ka hopena o ke kinotropic. ʻO kēia māhele e komo ana i nā beta-blockers a me nā mea anuanu kālepa. Ua kohoʻia lākou i kēlā me kēia maʻamau, a ua hāʻawiʻia ka lawelaweʻana no kekahi manawa lōʻihi (a hiki i ka loaʻaʻana o ke ola holoʻokoʻa), i kēia mau lā e ho'āʻo ana nā kauka e hoʻolako i nā lāʻau me nā hopena pilikia iki. Ua hoʻohana muaʻiaʻo Anaprilin, a i kēia mau lā he nui nāʻano likeʻole o ka hanauna hou.
Eia kekahi, hoʻohanaʻia nā lāʻau a me nā mea'alokulo e like me nā mea maʻamau.