ʻO ka Hypertrophic cardiomyopathy

ʻO ka maʻi, ka mea e hoʻonui i ka paia o ka hema, a ma nā meaʻoi loa o ka ventricle pono o ka puʻuwai, ua kapaʻiaʻo ka cardiomyopathy hypertension (HCMC). I loko o kēia maʻi, hoʻomāhuahua ka nui o nā hihia maʻamau, a no laila keʻeha mau nei ka septum hihia.

Manaʻoʻia he maʻi kēia o nā mea pāʻani - no ka hoʻonuiʻana i ka ikaika e hanaʻia ai ka maʻi koko. Uaʻike mua mākou i kekahi mau hihia i ka wā i make ai nā kānaka pāʻani ma ke kahua pāʻani ma muli o keʻano o ka maʻi cardiomyopathy - ka mea hoʻokani pôpeku Hungarianʻo Miklos Feher a me ka meaʻelimaʻo Jesse Marunde.

I loko o kēia maʻi, he wahi chaotic ka paʻakai i loko o ka myocardium, kahi e pili ana i ka hoʻohuiʻiaʻana o ka hua.

Nāʻano o ka maʻi o ke koko

I kēia lā,ʻikeʻia nā kauka e 3 mauʻano o ke kāpikipipiki o ke koko:

  1. Palekana Basal - hoʻonui ka hoʻomaha ma mua o ka 30 mm Hg. Nā'Ōlelo.
  2. Ka lapaʻau o Labile - uaʻikeʻia nā hanu holoʻokoʻa o ka māmāʻokoʻa.
  3. Hoʻopilikia pa'ū - kahi māmā ma kahi mālie ma lalo o 30 mm Hg. Nā'Ōlelo.

ʻO kaʻaeʻana i ka hyperterpic cardiomyopathy e pili ana i kēia mauʻanoʻekolu o ka maʻi,ʻoiai heʻanoʻoʻoleʻaʻole keʻano o keʻano e hōʻikeʻia ana e ka māmā lahipine ma lalo o 30 mm Hg. Nā'Ōlelo. ma kahi hoʻomaha a hoʻonāukiuki.

Nā hōʻailona o ka hypertrophic cardiomyopathy

Hōʻalowale ka Symptomatic o ka hypertrophic cardiomyopathy - ma kahi o 30% o nā mea maʻi e hanaʻole i nā hoʻopiʻi, i ia manawa e lilo koke ka make i ka hōʻike wale nō o ka maʻi. Ma kahi kūlana kūikawā, he mau'ōpiopio'ōpiopio iʻole e nānā i ka hoʻopiʻi, koe wale no ka hoʻopilikia o ka naʻau.

ʻO kēia maʻi ka mea i kapaʻia e ka maʻi liʻiliʻi liʻiliʻi - ma kēia hihia, kaʻehaʻeha, kaʻuʻuku o ka hanu a me ka uhuki, a me nā hanana angina .

Eia kekahi, me keʻano o ka cardiomyopathy hypertrophy, hiki i nā hōʻike o ka hāʻuleʻole o ka puʻuwai ventricular hema, e hiki ai ke ulu i ka hanu naʻauʻole.

ʻO nā hemahema i ke kani o ka puʻuwai e hiki ai ke hōʻeha . ʻO ka manawa kēia he mau extrasystoles ventricular a me paroxysms o ka tachycardia ventricular.

I nā hihia maʻamau, hiki i nā maʻi ke loaʻa i ka maʻi endocarditis a me ka thromboembolism.

ʻO ka hōʻoiaʻana o ka hypertrophic cardiomyopathy

Ma waho o nāʻano likeʻole o ka cardiomyopathy, uaʻikeʻia kaʻano maʻalahi o ka pepa hypertrophic ma muli o ka hōʻaiaʻana: no ka hōʻoiaʻana o ka hōʻailona,ʻoi aku ka nui o ka myocardial ma mua o ka 1.5 cm a me ka waihoʻana o ka maʻi hemahema (left impairment).

Ke nānāʻia, hiki i ka mea maʻi ke hoʻonui i ka palena o ka naʻau i ka hema, a i ka wā e paʻiʻia, loheʻia ka leo (systolic rhomboid).

Ma waena o nāʻano'ē aʻe o ke aʻoʻana i kēia mauʻano pilikino, penei:

ʻO keʻano o keʻano o ka maʻi

ʻO ka hōʻailona a me ka mālamaʻana i ka maʻi diabolic cardiomyopathy e pili pono ana ia e pale ai i ka hopena hopena. Ma hope o ka noʻonoʻoʻana i ka hōʻailona o ka maʻi, inā loaʻa kahi hopena hopena, hanaʻia ka hana maʻalahi. Ināʻaʻohe makehewa make, aʻaʻohe hōʻailona 'ōleloʻia, a laila,ʻaʻole i hoʻokōʻia nā hana kūikawā.

No ka mālamaʻana, he mea nui ka kaohiʻana i ke kino, a me ka hoʻohanaʻana i nā lāʻau lapaʻau me ka hopena o ke kinotropic. ʻO kēia māhele e komo ana i nā beta-blockers a me nā mea anuanu kālepa. Ua kohoʻia lākou i kēlā me kēia maʻamau, a ua hāʻawiʻia ka lawelaweʻana no kekahi manawa lōʻihi (a hiki i ka loaʻaʻana o ke ola holoʻokoʻa), i kēia mau lā e ho'āʻo ana nā kauka e hoʻolako i nā lāʻau me nā hopena pilikia iki. Ua hoʻohana muaʻiaʻo Anaprilin, a i kēia mau lā he nui nāʻano likeʻole o ka hanauna hou.

Eia kekahi, hoʻohanaʻia nā lāʻau a me nā mea'alokulo e like me nā mea maʻamau.